Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000601410 | SCV000711792 | uncertain significance | not specified | 2016-04-12 | criteria provided, single submitter | clinical testing | The p.Arg2335Trp variant in OTOG has not been previously reported in individuals with hearing loss, but has been identified in 2/7658 of South Asian chromosomes by the Exome Aggregation Consortium (ExAC, http://exac.broadinstitute.org; dbSN P rs755149839). Although this variant has been seen in the general population, i ts frequency is not high enough to rule out a pathogenic role. Computational pre diction tools and conservation analyses do not provide strong support for or aga inst an impact to the protein. In summary, the clinical significance of the p.Ar g2335Trp variant is uncertain. |
Division of Human Genetics, |
RCV000185566 | SCV000238457 | uncertain significance | Autosomal recessive nonsyndromic hearing loss 18B | 2015-02-03 | no assertion criteria provided | research | This variant (NM_001277269.1:c.7003C>T;p.R2335W) is considered a variant of uncertain significance, as it has not been reported in the literature; however, it was seen in 2 alleles out of 17,984 alleles in ExAC with no homozygotes. It occurs in a highly conserved amino acid position and does not occur in a functional domain. |