Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001560828 | SCV001783314 | likely pathogenic | not provided | 2020-01-06 | criteria provided, single submitter | clinical testing | Intronic +5 splice site variant in a gene for which loss-of-function is a known mechanism of disease, and both in silico predictors and evolutionary conservation support a deleterious effect; Not observed in large population cohorts (Lek et al., 2016); Has not been previously published as pathogenic or benign to our knowledge |
Genome |
RCV000845042 | SCV000986880 | not provided | Seizure; Intellectual disability; Developmental delay | no assertion provided | phenotyping only | Variant interpretted as Likely pathogenic and reported on 01-09-2020 by Lab or GTR ID 26957. GenomeConnect assertions are reported exactly as they appear on the patient-provided report from the testing laboratory. GenomeConnect staff make no attempt to reinterpret the clinical significance of the variant. | |
Cologne Center for Genomics, |
RCV002221588 | SCV002498745 | pathogenic | Poirier-Bienvenu neurodevelopmental syndrome | 2022-04-11 | no assertion criteria provided | research |