Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Suma Genomics | RCV005215801 | SCV005687491 | pathogenic | Developmental and epileptic encephalopathy, 2 | criteria provided, single submitter | clinical testing | A splice variant c.2152+1G>C (g.18609571G>C) is observed in intron 14 of CDKL5 in heterozygous state. This variant is not observed in the gnomAD database. In-silico analysis tool SpliceAI predicts this variant in CDKL5 to cause aberrant splicing. ACMG criteria met: PVS1:Null variant in a gene where the loss of function is a known mechanism of disease PM6: De novo variant PM2_Supporting: Extremely low frequency in gnomAD population databases |