Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001567802 | SCV001791552 | uncertain significance | not provided | 2019-12-06 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; Not observed at a significant frequency in large population cohorts (Lek et al., 2016); In silico analysis, which includes splice predictors and evolutionary conservation, suggests this variant may impact gene splicing. In the absence of RNA/functional studies, the actual effect of this sequence change is unknown.; In silico analysis, which includes splice predictors and evolutionary conservation, supports that the missense change does not alter protein structure/function |
Prevention |
RCV004536199 | SCV004113745 | uncertain significance | NRXN1-related disorder | 2022-12-21 | criteria provided, single submitter | clinical testing | The NRXN1 c.259G>T variant is predicted to result in the amino acid substitution p.Ala87Ser. This variant was reported in an individual with an unspecified neurodevelopmental disorder (Supplementary Table 5, Wang et al 2020. PubMed ID: 33004838). This variant is reported in 0.00090% of alleles in individuals of European (Non-Finnish) descent in gnomAD (http://gnomad.broadinstitute.org/variant/2-50573829-C-A). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |