Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV003313027 | SCV004012247 | pathogenic | not provided | 2023-01-05 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect on KDM5C transactivation activity (Poeta et al., 2019); Nonsense variant predicted to result in protein truncation, as the last 53 amino acids are lost, and other loss-of-function variants have been reported downstream in HGMD; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 34992252, 31691806, 19377476) |
OMIM | RCV000010416 | SCV000030642 | pathogenic | Intellectual disability, X-linked 97 | 2009-05-01 | no assertion criteria provided | literature only |