Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003141264 | SCV003823043 | uncertain significance | Neurodegeneration, childhood-onset, with cerebellar atrophy | 2022-03-29 | criteria provided, single submitter | clinical testing | |
Clinical Genomics Laboratory, |
RCV003141264 | SCV005688760 | uncertain significance | Neurodegeneration, childhood-onset, with cerebellar atrophy | 2024-09-15 | criteria provided, single submitter | clinical testing | The AGTPBP1 c.3206G>T (p.Cys1069Phe) variant, to our knowledge, has not been reported in the medical literature. The highest population minor allele frequency in the population database genome aggregation database (v.2.1.1) is 0.17% in the African population. Computational predictors suggest that the variant does not impact AGTPBP1 function. This variant has been reported in the ClinVar database as a germline variant of uncertain significance by one submitter. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |