Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000485794 | SCV000573020 | pathogenic | not provided | 2019-05-09 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed in large population cohorts (Lek et al., 2016); Has not been previously published as pathogenic or benign to our knowledge |
Centogene AG - |
RCV001251101 | SCV001426600 | likely pathogenic | DYRK1A-related intellectual disability syndrome | criteria provided, single submitter | clinical testing | ||
Labcorp Genetics |
RCV001251101 | SCV002238504 | pathogenic | DYRK1A-related intellectual disability syndrome | 2021-10-24 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 423335). This sequence change creates a premature translational stop signal (p.Lys191Thrfs*6) in the DYRK1A gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in DYRK1A are known to be pathogenic (PMID: 25944381). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with clinical features of DYRK1A-related conditions (PMID: 32860008). |
Ce |
RCV000485794 | SCV005050374 | pathogenic | not provided | 2024-05-01 | criteria provided, single submitter | clinical testing | DYRK1A: PVS1, PM2, PM6, PS4:Moderate |
Genome |
RCV001265303 | SCV001443420 | pathogenic | Complex neurodevelopmental disorder | 2018-09-10 | no assertion criteria provided | provider interpretation | Submission from Simons Searchlight facilitated by GenomeConnect. Variant interpreted by the Simons Searchlight team most recently on 2018-09-10 and interpreted as Pathogenic. The reporting laboratory might also submit to ClinVar. This variant was identified in multiple probands enrolled in Simons Searchlight. |