Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004785872 | SCV005400966 | uncertain significance | Clark-Baraitser syndrome | 2023-06-22 | criteria provided, single submitter | clinical testing | The missense variant c.2071G>A(p.Val691Ile) in TRIP12 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The observed variant is absent in gnomAD exomes database. This variant has not been submitted to the ClinVar database. Multiple lines of computational evidence (Polyphen - possibly damaging, SIFT - tolerated and MutationTaster - disease causing) predicts conflicting evidence on protein structure and function for this variant. The reference amino acid change p.Val691Ile in TRIP12 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Val at position 691 is changed to a Ile changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Uncertain Significance (VUS). |