Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Medical Genetics, |
RCV004596020 | SCV005090996 | pathogenic | Clark-Baraitser syndrome | 2024-07-12 | criteria provided, single submitter | clinical testing | PVS1, PS2, PM2 -The variant is expected to result in an absent or disrupted protein product. Not observed in large population cohorts (gnomAD). The variant was detected de novo (paternity confirmed). |