Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001682945 | SCV001898881 | benign | not provided | 2021-02-17 | criteria provided, single submitter | clinical testing | This variant is associated with the following publications: (PMID: 33337535) |
Fulgent Genetics, |
RCV002503922 | SCV002809502 | likely benign | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities | 2022-01-18 | criteria provided, single submitter | clinical testing | |
Molecular Genetics, |
RCV002503922 | SCV004812811 | benign | Neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities | 2023-05-04 | criteria provided, single submitter | clinical testing | European Non-Finnish population allele frequency is 77.92% (rs779500270, 8811/11110 alleles, 3564 homozygotes in gnomAD v2.1). Based on the classification scheme RMH Modified ACMG/AMP Guidelines v1.4.0, this variant is classified as BENIGN. Following criteria are met: BA1 |
CHU Sainte- |
RCV000240501 | SCV000299198 | uncertain significance | Oromandibular-limb hypogenesis spectrum | 2016-08-12 | no assertion criteria provided | research |