Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Equipe Genetique des Anomalies du Developpement, |
RCV000984032 | SCV000930642 | pathogenic | Primrose syndrome | 2019-06-16 | criteria provided, single submitter | clinical testing | |
Diagnostic Laboratory, |
RCV001260823 | SCV001437919 | pathogenic | Intellectual disability | 2020-09-10 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001873236 | SCV002130283 | uncertain significance | not provided | 2021-06-25 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive, but these predictions have not been confirmed by published functional studies and their clinical significance is uncertain. This variant has not been reported in the literature in individuals with ZBTB20-related conditions. ClinVar contains an entry for this variant (Variation ID: 638662). This variant is not present in population databases (ExAC no frequency). This sequence change replaces serine with arginine at codon 647 of the ZBTB20 protein (p.Ser647Arg). The serine residue is highly conserved and there is a moderate physicochemical difference between serine and arginine. |