Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001175604 | SCV001339255 | pathogenic | Intellectual disability-severe speech delay-mild dysmorphism syndrome | 2024-02-21 | criteria provided, single submitter | clinical testing | Variant summary: FOXP1 c.659dupC (p.Gln221SerfsX74) results in a premature termination codon, predicted to cause a truncation of the encoded protein or absence of the protein due to nonsense mediated decay, which are commonly known mechanisms for disease. The variant was absent in 251050 control chromosomes (gnomAD). To our knowledge, no occurrence of c.659dupC in individuals affected with Mental Retardation With Language Impairment And With Or Without Autistic Features and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 918163). Based on the evidence outlined above, the variant was classified as pathogenic. |