Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001262584 | SCV001440511 | pathogenic | Dyggve-Melchior-Clausen syndrome | 2019-01-01 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004035398 | SCV004107924 | likely pathogenic | DYM-related disorder | 2023-01-09 | criteria provided, single submitter | clinical testing | The DYM c.947-2A>G variant is predicted to disrupt the AG splice acceptor site and interfere with normal splicing. To our knowledge, this variant has not been reported in the literature or a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Variants that disrupt the consensus splice acceptor site in DYM are expected to be pathogenic. This variant is interpreted as likely pathogenic. |