Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003340828 | SCV004047587 | likely pathogenic | Hereditary spherocytosis type 2 | criteria provided, single submitter | clinical testing | The c.647+1G>A splice site variant in SPTB gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The c.647+1G>A variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. Loss of function variants have been previously reported to be disease causing. For these reasons, this variant has been classified as Likely Pathogenic. |