Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001930310 | SCV002183316 | uncertain significance | Sulfite oxidase deficiency due to molybdenum cofactor deficiency type A | 2021-08-05 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. This variant has not been reported in the literature in individuals affected with MOCS1-related conditions. This sequence change replaces glycine with valine at codon 299 of the MOCS1 protein (p.Gly299Val). The glycine residue is highly conserved and there is a moderate physicochemical difference between glycine and valine. |