Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Dunham Lab, |
RCV002305773 | SCV002599346 | pathogenic | Anemia, nonspherocytic hemolytic, due to G6PD deficiency | 2022-08-12 | criteria provided, single submitter | curation | Variant found in hemizygotes with deficiency and CNSHA (PP4). For one, mother is heterozygous and has decreased G6PD activity (PP1); for other, variant not found in mother so assumed de novo (PM6). Decreased activity in red blood cells (0-23%) (PS3). Not found in gnomAD (PM2). Post_P 0.994 (odds of pathogenicity 1517, Prior_P 0.1). |