Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000531545 | SCV000652615 | benign | Combined immunodeficiency due to LRBA deficiency | 2024-01-25 | criteria provided, single submitter | clinical testing | |
New York Genome Center | RCV000531545 | SCV002097924 | uncertain significance | Combined immunodeficiency due to LRBA deficiency | 2021-03-04 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV002222550 | SCV002500390 | uncertain significance | not specified | 2022-03-14 | criteria provided, single submitter | clinical testing | Variant summary: LRBA c.2674G>A (p.Ala892Thr) results in a non-conservative amino acid change in the encoded protein sequence. Three of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 0.0012 in 251260 control chromosomes in the gnomAD database, including 1 homozygotes. This frequency does not allow conclusions about variant significance. c.2674G>A has been reported in the literature in an individual affected with Common Variable Immunodeficiency, without strong evidence for causality (Maffucci_2016). This report does not provide unequivocal conclusions about association of the variant with Common Variable Immunodeficiency 8, With Autoimmunity. To our knowledge, no experimental evidence demonstrating an impact on protein function has been reported. Two clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014 without evidence for independent evaluation. One laboratory classified the variant as benign, and one laboratory classified the variant as uncertain significance. Based on the evidence outlined above, the variant was classified as uncertain significance. |
Ce |
RCV003333996 | SCV004042208 | benign | not provided | 2023-09-01 | criteria provided, single submitter | clinical testing | LRBA: BS1, BS2 |