Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002251055 | SCV002521426 | uncertain significance | Combined immunodeficiency due to LRBA deficiency | 2022-05-22 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. Protein truncation variants are a common disease-causing mechanism. Therefore, this variant is classified as uncertain significanceaccording to the recommendation of ACMG/AMP guideline. |