Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003337828 | SCV004048176 | uncertain significance | Combined immunodeficiency due to LRBA deficiency | criteria provided, single submitter | clinical testing | The missense variant in c.7031C>T(p.Ser2344Phe) in LRBA gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Ser2344Phe variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. The amino acid Ser at position 2344 is changed to a Phe changing protein sequence and it might alter its composition and physico-chemical properties. The residue is conserved across species. The amino acid change p.Ser2344Phe in LRBA is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |