Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000395243 | SCV000335813 | uncertain significance | not provided | 2015-09-29 | criteria provided, single submitter | clinical testing | |
Institute of Human Genetics Munich, |
RCV002468573 | SCV002764752 | likely pathogenic | Global developmental delay; EEG abnormality; Exaggerated startle response | 2021-03-05 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003743695 | SCV004559341 | uncertain significance | Charcot-Marie-Tooth disease type 2 | 2023-06-11 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 283613). This variant has not been reported in the literature in individuals affected with KIF1B-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Arg981*) in the KIF1B gene. It is expected to result in an absent or disrupted protein product. However, the current clinical and genetic evidence is not sufficient to establish whether loss-of-function variants in KIF1B cause disease. |