Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics Laboratory, |
RCV001174217 | SCV001337344 | uncertain significance | Charcot-Marie-Tooth disease | criteria provided, single submitter | clinical testing | ||
Ambry Genetics | RCV004032972 | SCV002606381 | uncertain significance | not specified | 2024-06-14 | criteria provided, single submitter | clinical testing | The p.P1031S variant (also known as c.3091C>T), located in coding exon 27 of the KIF1B gene, results from a C to T substitution at nucleotide position 3091. The proline at codon 1031 is replaced by serine, an amino acid with similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |