Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004719313 | SCV005325178 | uncertain significance | not provided | 2024-02-16 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect: I65M may operate through a gain-of-function mechanism that disrupts cellular osmoregulation (PMID: 38334649); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Reported using an alternate transcript of the gene; This variant is associated with the following publications: (PMID: 38334649, 25090642) |
OMIM | RCV003152306 | SCV003840894 | pathogenic | Cataract 50 with or without glaucoma | 2023-08-02 | no assertion criteria provided | literature only |