Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV000282947 | SCV000399259 | uncertain significance | Brittle cornea syndrome 1 | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Ce |
RCV000761944 | SCV000892171 | likely benign | not provided | 2024-02-01 | criteria provided, single submitter | clinical testing | ZNF469: BP4 |
Genome Diagnostics Laboratory, |
RCV002278432 | SCV002565398 | uncertain significance | Ehlers-Danlos syndrome | 2022-04-08 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002379198 | SCV002670272 | likely benign | Cardiovascular phenotype | 2021-07-16 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Genome Diagnostics Laboratory, |
RCV000761944 | SCV001977709 | likely benign | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV000761944 | SCV001979937 | likely benign | not provided | no assertion criteria provided | clinical testing | ||
Prevention |
RCV004751459 | SCV005345733 | likely benign | ZNF469-related disorder | 2024-07-01 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |