Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV002211369 | SCV002497951 | uncertain significance | not provided | 2022-03-01 | criteria provided, single submitter | clinical testing | |
Genome Diagnostics Laboratory, |
RCV002277043 | SCV002565401 | uncertain significance | Ehlers-Danlos syndrome | 2021-10-12 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002391370 | SCV002675096 | uncertain significance | Cardiovascular phenotype | 2021-05-21 | criteria provided, single submitter | clinical testing | The p.R2504M variant (also known as c.7511G>T), located in coding exon 2 of the ZNF469 gene, results from a G to T substitution at nucleotide position 7511. The arginine at codon 2504 is replaced by methionine, an amino acid with similar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV002211369 | SCV003491064 | likely benign | not provided | 2024-12-16 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV003485768 | SCV004237790 | uncertain significance | Brittle cornea syndrome 1 | 2023-12-19 | criteria provided, single submitter | clinical testing |