Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000479226 | SCV000567010 | pathogenic | not provided | 2015-07-14 | criteria provided, single submitter | clinical testing | The W37X variant in the MAGT1 gene has not been reported previously as a pathogenic variant nor as a benign polymorphism, to our knowledge. This variant is predicted to cause loss ofnormal protein function either through protein truncation or nonsense-mediated mRNA decay. TheW37X variant was not observed in approximately 6,500 individuals of European and AfricanAmerican ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benignvariant in these populations. We interpret W37X as a pathogenic variant. |
OMIM | RCV000850121 | SCV000992285 | pathogenic | X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection and neoplasia | 2019-08-26 | no assertion criteria provided | literature only |