Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000331517 | SCV000330626 | pathogenic | not provided | 2016-12-28 | criteria provided, single submitter | clinical testing | The c.621delA variant in the COL13A1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The c.621delA variant causes a frameshift starting with codon Glycine 208, changes this amino acid to a Glutamic Acid residue, and creates a premature Stop codon at position 15 of the new reading frame, denoted p.Gly208GlufsX15. This variant is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. We interpret c.621delA as a pathogenic variant. |
Revvity Omics, |
RCV003492024 | SCV004235040 | pathogenic | Congenital myasthenic syndrome 19 | 2023-03-15 | criteria provided, single submitter | clinical testing |