Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000206124 | SCV000259649 | likely benign | Primary ciliary dyskinesia | 2024-10-22 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000669663 | SCV000794439 | uncertain significance | Primary ciliary dyskinesia 3 | 2017-09-26 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000206124 | SCV002663090 | uncertain significance | Primary ciliary dyskinesia | 2020-03-09 | criteria provided, single submitter | clinical testing | The p.R4127C variant (also known as c.12379C>T), located in coding exon 72 of the DNAH5 gene, results from a C to T substitution at nucleotide position 12379. The arginine at codon 4127 is replaced by cysteine, an amino acid with highly dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Natera, |
RCV000206124 | SCV001462292 | uncertain significance | Primary ciliary dyskinesia | 2020-09-16 | no assertion criteria provided | clinical testing |