Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002435228 | SCV002748476 | uncertain significance | Primary ciliary dyskinesia | 2022-06-12 | criteria provided, single submitter | clinical testing | The p.L95F variant (also known as c.283C>T), located in coding exon 4 of the DNAH5 gene, results from a C to T substitution at nucleotide position 283. The leucine at codon 95 is replaced by phenylalanine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Mayo Clinic Laboratories, |
RCV004790211 | SCV005411778 | uncertain significance | not provided | 2024-03-20 | criteria provided, single submitter | clinical testing | BP4 |
Fulgent Genetics, |
RCV005032277 | SCV005671063 | uncertain significance | Primary ciliary dyskinesia 3 | 2023-12-29 | criteria provided, single submitter | clinical testing |