Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000536018 | SCV000624240 | benign | Primary ciliary dyskinesia | 2024-09-06 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000536018 | SCV002749980 | uncertain significance | Primary ciliary dyskinesia | 2023-10-31 | criteria provided, single submitter | clinical testing | The p.R982C variant (also known as c.2944C>T), located in coding exon 19 of the DNAH5 gene, results from a C to T substitution at nucleotide position 2944. The arginine at codon 982 is replaced by cysteine, an amino acid with highly dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Natera, |
RCV000536018 | SCV002081768 | uncertain significance | Primary ciliary dyskinesia | 2021-01-05 | no assertion criteria provided | clinical testing |