Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000691815 | SCV000819608 | benign | Primary ciliary dyskinesia | 2023-12-21 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000691815 | SCV002661405 | uncertain significance | Primary ciliary dyskinesia | 2021-10-29 | criteria provided, single submitter | clinical testing | The p.S211L variant (also known as c.632C>T), located in coding exon 5 of the DNAH5 gene, results from a C to T substitution at nucleotide position 632. The serine at codon 211 is replaced by leucine, an amino acid with dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Ce |
RCV003432737 | SCV004153961 | uncertain significance | not provided | 2022-06-01 | criteria provided, single submitter | clinical testing | DNAH5: PM2, BP4 |
Gene |
RCV003432737 | SCV005389114 | uncertain significance | not provided | 2024-03-08 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Natera, |
RCV000691815 | SCV002081821 | uncertain significance | Primary ciliary dyskinesia | 2019-10-28 | no assertion criteria provided | clinical testing | |
Prevention |
RCV004742577 | SCV005351644 | uncertain significance | DNAH5-related disorder | 2024-05-02 | no assertion criteria provided | clinical testing | The DNAH5 c.632C>T variant is predicted to result in the amino acid substitution p.Ser211Leu. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.040% of alleles in individuals of Latino descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |