Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003081301 | SCV003456898 | benign | Primary ciliary dyskinesia | 2024-02-06 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003081301 | SCV005573151 | uncertain significance | Primary ciliary dyskinesia | 2024-07-24 | criteria provided, single submitter | clinical testing | The p.A2534V variant (also known as c.7601C>T), located in coding exon 45 of the DNAH5 gene, results from a C to T substitution at nucleotide position 7601. The alanine at codon 2534 is replaced by valine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |