Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000521389 | SCV000620863 | uncertain significance | not provided | 2017-09-25 | criteria provided, single submitter | clinical testing | The A67T variant in the ACAN gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The A67T variant is observed in 284/126674 (0.22%) alleles from individuals of European (Non-Finnish) background, in large population cohorts (Lek et al., 2016). The A67T variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs at a position that is not conserved. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. We interpret A67T as a variant of uncertain significance. |
Labcorp Genetics |
RCV000521389 | SCV002451519 | likely benign | not provided | 2025-01-23 | criteria provided, single submitter | clinical testing |