Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
MVZ Dr. |
RCV004698413 | SCV005196593 | likely pathogenic | Short stature and advanced bone age, with or without early-onset osteoarthritis and/or osteochondritis dissecans | criteria provided, single submitter | clinical testing | The variant c.2536_2537delinsA for p.(Pro846Thrfs*99) in ACAN leads to a shift in the reading frame and suggests a loss of function of the protein or premature degradation of the ACAN mRNA (nonsense me-diated RNA decay). It has not yet been described in the literature and databases and is not found in population databases of various ethnic groups. |