Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000795694 | SCV000935164 | likely benign | T-cell immunodeficiency, congenital alopecia, and nail dystrophy | 2023-12-08 | criteria provided, single submitter | clinical testing | |
Center for Genomics, |
RCV003224472 | SCV003919989 | uncertain significance | T-cell immunodeficiency, congenital alopecia, and nail dystrophy; T-cell lymphopenia, infantile, with or without nail dystrophy, autosomal dominant | 2022-10-04 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature but is present in the Genome Aggregation Database (Highest reported MAF 0.009% (4/41432) (https://gnomad.broadinstitute.org/variant/17-28534453-G-A?dataset=gnomad_r3). This variant is present in ClinVar (Variation ID:642263). Evolutionary conservation and computational predictive tools for this variant are limited or unavailable. Of note, this variant is a silent variant and does not change the amino acid, reducing the probability that this variant is disease causing. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. |
Breakthrough Genomics, |
RCV004693265 | SCV005192784 | uncertain significance | not provided | criteria provided, single submitter | not provided |