Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001374631 | SCV001571227 | likely pathogenic | Intellectual disability, autosomal dominant 30 | 2021-04-13 | no assertion criteria provided | clinical testing | de novo variant in an individual with Seizure/epilepsy/Rx: Focal dyscognitive seizures, onset 5 years. LEV effective. EEG: Occasional spike and wave discharges mid and left parietal region.Neuropsych/development: ASD, moderate LD, aggressive behaviour; hypotonia, abnormal gait, scoliosis, neurogenic bladder; MRI mild cerebellar tonsillar ectopia.Dysmorphism: NoneSomatic: Recurrent skin and respiratory infections; hypoplastic thoracic vertebra. |