Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000525912 | SCV000628054 | likely benign | Multiple endocrine neoplasia, type 1 | 2024-11-06 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001011715 | SCV001172070 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-09-02 | criteria provided, single submitter | clinical testing | The p.P493L variant (also known as c.1478C>T), located in coding exon 9 of the MEN1 gene, results from a C to T substitution at nucleotide position 1478. The proline at codon 493 is replaced by leucine, an amino acid with similar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV000525912 | SCV005060834 | uncertain significance | Multiple endocrine neoplasia, type 1 | 2023-12-24 | criteria provided, single submitter | clinical testing |