Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000470592 | SCV000541196 | likely benign | Multiple endocrine neoplasia, type 1 | 2024-11-15 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000491071 | SCV000579761 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-01-17 | criteria provided, single submitter | clinical testing | The p.R295W variant (also known as c.883C>T), located in coding exon 5 of the MEN1 gene, results from a C to T substitution at nucleotide position 883. The arginine at codon 295 is replaced by tryptophan, an amino acid with dissimilar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV000470592 | SCV000894653 | uncertain significance | Multiple endocrine neoplasia, type 1 | 2018-10-31 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003392263 | SCV004120502 | uncertain significance | MEN1-related disorder | 2023-05-24 | criteria provided, single submitter | clinical testing | The MEN1 c.898C>T variant is predicted to result in the amino acid substitution p.Arg300Trp. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.011% of alleles in individuals of African descent in gnomAD (http://gnomad.broadinstitute.org/variant/11-64574512-G-A). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |