Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV002281851 | SCV002572369 | uncertain significance | not specified | 2022-08-26 | criteria provided, single submitter | clinical testing | Variant summary: FGD4 c.-102624G>A is located in the untranscribed region upstream of the FGD4 gene region in transcript NM_139241.3, however it might affect a splice site in other transcripts (c.166+1G>A, in NM_001370298.3). The variant allele was found at a frequency of 0.00016 in 150938 control chromosomes (gnomAD v3.1.2). To our knowledge, no occurrence of c.-102624G>A in individuals affected with Charcot-Marie Disease Type 4H and no experimental evidence demonstrating its impact on protein function have been reported. No clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014. Based on the evidence outlined above, the variant was classified as uncertain significance. |