Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002814866 | SCV003198628 | uncertain significance | Neuronal ceroid lipofuscinosis 7 | 2022-10-13 | criteria provided, single submitter | clinical testing | This variant, c.1458_1459delinsAA, is a complex sequence change that results in the deletion and insertion of 2 different amino acid(s) in the MFSD8 protein (p.Ser486_Leu487delinsArgMet). Information on the frequency of this variant in the gnomAD database is not available, as this variant may be reported differently in the database. This variant has not been reported in the literature in individuals affected with MFSD8-related conditions. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |