Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000001058 | SCV001406037 | pathogenic | Neuronal ceroid lipofuscinosis 7 | 2024-10-24 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Tyr298*) in the MFSD8 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in MFSD8 are known to be pathogenic (PMID: 19177532, 25227500, 28586915). This variant is present in population databases (rs118203977, gnomAD 0.003%). This premature translational stop signal has been observed in individual(s) with neuronal ceroid lipofuscinosis (PMID: 17564970). ClinVar contains an entry for this variant (Variation ID: 1003). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. For these reasons, this variant has been classified as Pathogenic. |
Revvity Omics, |
RCV001781154 | SCV002024351 | pathogenic | not provided | 2022-12-21 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV005031377 | SCV005662940 | pathogenic | Neuronal ceroid lipofuscinosis 7; Macular dystrophy with central cone involvement | 2024-03-06 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000001058 | SCV000021208 | pathogenic | Neuronal ceroid lipofuscinosis 7 | 2007-07-01 | no assertion criteria provided | literature only |