Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002269511 | SCV002552783 | uncertain significance | not provided | 2022-07-18 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Ambry Genetics | RCV003355841 | SCV004055531 | uncertain significance | Inborn genetic diseases | 2023-09-13 | criteria provided, single submitter | clinical testing | The c.3782G>T (p.G1261V) alteration is located in exon 24 (coding exon 24) of the TCOF1 gene. This alteration results from a G to T substitution at nucleotide position 3782, causing the glycine (G) at amino acid position 1261 to be replaced by a valine (V). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Prevention |
RCV003896100 | SCV004709420 | likely benign | TCOF1-related disorder | 2023-05-08 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |