Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001291836 | SCV001480338 | likely pathogenic | Phelan-McDermid syndrome | 2020-11-17 | criteria provided, single submitter | clinical testing | The variant c.1871G>C, (p.(Ser624Thr)) in SHANK3-gene is not found in the gnomAD database. The mutation has not yet been described in the literature or listed in the databases HGMD and ClinVar databases. This variant has a pathogenic computational verdict based on in silico prediction programs (M-CAP, SIFT), but to our knowledge no functional characterization to determine the functional consequence of this substitution was performed as of yet. ACMG criteria used for classification: PVS1, PM2. |