Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV000625439 | SCV000745356 | uncertain significance | Hereditary sensory and autonomic neuropathy type 6 | 2017-12-11 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001347780 | SCV001542055 | uncertain significance | Hereditary sensory and autonomic neuropathy type 6; Epidermolysis bullosa simplex 3, localized or generalized intermediate, with BP230 deficiency | 2022-03-31 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. ClinVar contains an entry for this variant (Variation ID: 522339). This variant has not been reported in the literature in individuals affected with DST-related conditions. This variant is present in population databases (no rsID available, gnomAD 0.0009%). This sequence change replaces aspartic acid, which is acidic and polar, with glycine, which is neutral and non-polar, at codon 3393 of the DST protein (p.Asp3393Gly). The DST gene has multiple clinically relevant transcripts. This variant occurs in alternate transcript NM_015548.4, and corresponds to NM_001723.5:c.*89074A>G in the primary transcript. |
Clinical Genetics, |
RCV001700278 | SCV001925997 | uncertain significance | not provided | no assertion criteria provided | clinical testing |