Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV000625438 | SCV000745355 | uncertain significance | Hereditary sensory and autonomic neuropathy type 6 | 2016-05-02 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000801103 | SCV000940862 | likely benign | Hereditary sensory and autonomic neuropathy type 6; Epidermolysis bullosa simplex 3, localized or generalized intermediate, with BP230 deficiency | 2025-01-11 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002395638 | SCV002699210 | uncertain significance | Inborn genetic diseases | 2022-04-13 | criteria provided, single submitter | clinical testing | The p.N4694S variant (also known as c.14081A>G), located in coding exon 78 of the DST gene, results from an A to G substitution at nucleotide position 14081. The asparagine at codon 4694 is replaced by serine, an amino acid with highly similar properties. This amino acid position is well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Diagnostic Laboratory, |
RCV001529345 | SCV001742626 | uncertain significance | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics, |
RCV001529345 | SCV001923576 | uncertain significance | not provided | no assertion criteria provided | clinical testing | ||
Prevention |
RCV003905674 | SCV004724067 | likely benign | DST-related disorder | 2023-06-05 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |