Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000413516 | SCV000491415 | likely pathogenic | not provided | 2016-01-25 | criteria provided, single submitter | clinical testing | The G791S variant in the ARID1B gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The G791S variant was not observed in approximately 6500 individuals of European and African American ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in these populations. This substitution occurs at a position where amino acids with similar properties to Glycine are tolerated across species. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. The G791S variant is a strong candidate for a pathogenic variant. |
Baylor Genetics | RCV001336508 | SCV001529910 | likely pathogenic | Coffin-Siris syndrome 1 | 2018-01-29 | criteria provided, single submitter | clinical testing | This variant was determined to be likely pathogenic according to ACMG Guidelines, 2015 [PMID:25741868]. |
Baylor Genetics | RCV001533090 | SCV001748910 | likely pathogenic | ARID1B-related BAFopathy | 2021-06-10 | criteria provided, single submitter | clinical testing |