Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000596725 | SCV000704042 | pathogenic | not provided | 2016-12-07 | criteria provided, single submitter | clinical testing | |
Victorian Clinical Genetics Services, |
RCV002470920 | SCV002768954 | pathogenic | Coffin-Siris syndrome 1 | 2022-02-02 | criteria provided, single submitter | clinical testing | A heterozygous deletion and insertion variant was identified, NM_020732.3(ARID1B):c.3778_3780delinsAG in exon 15 of 20 of the ARID1B gene. This variant is predicted to cause a frameshift from amino acid position 1260 introducing a stop codon 5 residues downstream, NP_065783.3(ARID1B):p.(Tyr1260Serfs*5), resulting in loss of normal protein function through nonsense-mediated decay (NMD). The variant is not present in the gnomAD population database. It has been previously reported in a patient, however no clinical information is available (ClinVar). Other variants predicted to cause NMD have been reported as pathogenic in individuals with Coffin-Siris syndrome (ClinVar, HGMD®). Based on information available at the time of curation, this variant has been classified as PATHOGENIC. |