Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000520173 | SCV000621810 | uncertain significance | not provided | 2017-11-02 | criteria provided, single submitter | clinical testing | The P1687L variant in the DYNC2H1 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The P1687L variant is observed in 3/110970 (0.003%) alleles from individuals of non-Finnish European background, in large population cohorts (Lek et al., 2016). The P1687L variant is a semi-conservative amino acid substitution, which may impact secondary protein structure as these residues differ in some properties. This substitution occurs at a position that is conserved across species. In silico analysis predicts this variant is probably damaging to the protein structure/function. We interpret P1687L as a variant of uncertain significance. |