Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV000084520 | SCV002822403 | pathogenic | not provided | 2022-12-01 | criteria provided, single submitter | clinical testing | Criteria applied: PP1:Strong, PM2, PP4:Moderate, PS4:Moderate |
Invitae | RCV002513906 | SCV003442395 | pathogenic | Frontotemporal dementia | 2022-07-29 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 8 of the MAPT gene. It does not directly change the encoded amino acid sequence of the MAPT protein. This variant is not present in population databases (gnomAD no frequency). This variant has been observed in individuals with frontotemporal dementia (PMID: 16503405, 34274155; Invitae). It has also been observed to segregate with disease in related individuals. ClinVar contains an entry for this variant (Variation ID: 98212). Studies have shown that this variant is associated with altered splicing resulting in increase of 4R-tau to 3R-tau ratio (PMID: 16503405, 34274155). Other variant(s) that result in increase of 4R-tau to 3R-tau ratio have been determined to be pathogenic (PMID: 9641683, 26297556). This suggests that this variant may also be clinically significant and likely to be disease-causing. For these reasons, this variant has been classified as Pathogenic. |
VIB Department of Molecular Genetics, |
RCV000084520 | SCV000116656 | not provided | not provided | no assertion provided | not provided |