Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003338217 | SCV004047240 | uncertain significance | Gordon syndrome | criteria provided, single submitter | clinical testing | The missense variant c.3193G>T (p.Asp1065Tyr) in PIEZO2 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Asp1065Tyr variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes and allele frequency of 0.003187% is reported in gnomAD. The amino acid Asp at position 1065 is changed to a Tyr changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Asp1065Tyr in PIEZO2 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |