Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001753403 | SCV001988371 | pathogenic | not provided | 2024-05-01 | criteria provided, single submitter | clinical testing | Identified in a patient with HDAC4-related brachydactyly and neurodevelopmental spectrum disorder (PMID: 20691407); Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 20691407) |
OMIM | RCV000005373 | SCV000025553 | uncertain significance | Chromosome 2q37 deletion syndrome | 2014-07-01 | no assertion criteria provided | literature only |